The Adult Cystic Fibrosis Center is available for both outpatient and inpatient needs and provides care in several settings, including the Pulmonary Function Test Lab at University Hospital, the Medical Specialty Clinic at University Physicians Medical Building and the Springfield outreach clinic.
Cystic Fibrosis is an inherited disease that primarily affects the respiratory (lungs and sinuses) and digestive systems. It is caused by gene mutations that cause mucus in the body to build up and affect many body organs. Symptoms of the disease can range from mild to severe. The disease was first described in 1938. The sweat test was developed in 1953 by Dr. Paul di Sant’Agnese when he recognized salt loss as the cause of death in cystic fibrosis patients during a heat wave in New York City. Cystic fibrosis remains one of the most common life-shortening genetic diseases in the United States.
Advances in care
Enormous technologic advances have been made in both disease diagnosis and treatment over the past several decades, resulting in improved survival among patients. Medical, social and nutritional needs of patients with cystic fibrosis often change as they mature. Fertility issues and parenting also become important issues for cystic fibrosis patients. For this reason, the Cystic Fibrosis Foundation has asked that the accredited cystic fibrosis care centers develop adult-centered care sites.
Treatment for related conditions
MU Health Care treats other conditions related to cystic fibrosis, including: